Central neurocytoma is a very rare brain tumor of young adults (over 100 cases reported worldwide). It is typically found in the lateral ventricles and occasionally in the third ventricle. Symptoms ar...
Comprehensive, easy-to-understand information about this condition
How we create this content →The limited documentation surrounding central neurocytoma reflects its rarity, as it affects fewer than 100 individuals per year globally. This rarity hampers extensive clinical studies and comprehensive data collection. Furthermore, the absence of identified genetic factors and inheritance patterns complicates the understanding of the disease, leaving many questions unanswered. Despite these challenges, ongoing research may illuminate further insights into this condition.
The clinical features of central neurocytoma primarily include hydrocephalus, which is always present, and abnormal lateral ventricle morphology, seen in 80-99% of cases. Other common symptoms include intracranial cystic lesions, abnormal cellular phenotypes, nausea and vomiting, headaches, and visual abnormalities, with varying frequencies between 30-79%. These symptoms are indicative of increased intracranial pressure and highlight the need for prompt diagnosis and treatment.
To navigate your care effectively, seek a neurosurgeon with experience in treating brain tumors, particularly central neurocytomas. It may also be beneficial to consult with a neuro-oncologist who specializes in brain tumors. While no patient organizations are currently identified, you can explore resources such as the Genetic and Rare Diseases Information Center (GARD) at rarediseases.info.nih.gov for additional support and information. Participating in clinical trials could also be a valuable opportunity for accessing new treatments.
Currently, there are two active clinical trials focusing on central neurocytoma. These trials may offer potential treatment options and contribute to the understanding of the disease. For more information on these trials, you can visit ClinicalTrials.gov and search for 'central neurocytoma'. Engaging in clinical trials may provide access to cutting-edge therapies and contribute to advancing knowledge about this rare tumor.
Actionable guidance for navigating care for central neurocytoma
To navigate your care effectively, seek a neurosurgeon with experience in treating brain tumors, particularly central neurocytomas. It may also be beneficial to consult with a neuro-oncologist who specializes in brain tumors. While no patient organizations are currently identified, you can explore resources such as the Genetic and Rare Diseases Information Center (GARD) at rarediseases.info.nih.gov for additional support and information. Participating in clinical trials could also be a valuable opportunity for accessing new treatments.
Consider asking your healthcare providers these condition-specific questions
Helpful links for rare disease information and support
The limited documentation surrounding central neurocytoma reflects its rarity, as it affects fewer than 100 individuals per year globally. This rarity hampers extensive clinical studies and comprehensive data collection. Furthermore, the absence of identified genetic factors and inheritance patterns complicates the understanding of the disease, leaving many questions unanswered. Despite these challenges, ongoing research may illuminate further insights into this condition.
The clinical features of central neurocytoma primarily include hydrocephalus, which is always present, and abnormal lateral ventricle morphology, seen in 80-99% of cases. Other common symptoms include intracranial cystic lesions, abnormal cellular phenotypes, nausea and vomiting, headaches, and visual abnormalities, with varying frequencies between 30-79%. These symptoms are indicative of increased intracranial pressure and highlight the need for prompt diagnosis and treatment.
To navigate your care effectively, seek a neurosurgeon with experience in treating brain tumors, particularly central neurocytomas. It may also be beneficial to consult with a neuro-oncologist who specializes in brain tumors. While no patient organizations are currently identified, you can explore resources such as the Genetic and Rare Diseases Information Center (GARD) at rarediseases.info.nih.gov for additional support and information. Participating in clinical trials could also be a valuable opportunity for accessing new treatments.
Currently, there are two active clinical trials focusing on central neurocytoma. These trials may offer potential treatment options and contribute to the understanding of the disease. For more information on these trials, you can visit ClinicalTrials.gov and search for 'central neurocytoma'. Engaging in clinical trials may provide access to cutting-edge therapies and contribute to advancing knowledge about this rare tumor.
Actionable guidance for navigating care for central neurocytoma
To navigate your care effectively, seek a neurosurgeon with experience in treating brain tumors, particularly central neurocytomas. It may also be beneficial to consult with a neuro-oncologist who specializes in brain tumors. While no patient organizations are currently identified, you can explore resources such as the Genetic and Rare Diseases Information Center (GARD) at rarediseases.info.nih.gov for additional support and information. Participating in clinical trials could also be a valuable opportunity for accessing new treatments.
Consider asking your healthcare providers these condition-specific questions
Helpful links for rare disease information and support
The limited documentation surrounding central neurocytoma reflects its rarity, as it affects fewer than 100 individuals per year globally. This rarity hampers extensive clinical studies and comprehensive data collection. Furthermore, the absence of identified genetic factors and inheritance patterns complicates the understanding of the disease, leaving many questions unanswered. Despite these challenges, ongoing research may illuminate further insights into this condition.
The clinical features of central neurocytoma primarily include hydrocephalus, which is always present, and abnormal lateral ventricle morphology, seen in 80-99% of cases. Other common symptoms include intracranial cystic lesions, abnormal cellular phenotypes, nausea and vomiting, headaches, and visual abnormalities, with varying frequencies between 30-79%. These symptoms are indicative of increased intracranial pressure and highlight the need for prompt diagnosis and treatment.
To navigate your care effectively, seek a neurosurgeon with experience in treating brain tumors, particularly central neurocytomas. It may also be beneficial to consult with a neuro-oncologist who specializes in brain tumors. While no patient organizations are currently identified, you can explore resources such as the Genetic and Rare Diseases Information Center (GARD) at rarediseases.info.nih.gov for additional support and information. Participating in clinical trials could also be a valuable opportunity for accessing new treatments.
Currently, there are two active clinical trials focusing on central neurocytoma. These trials may offer potential treatment options and contribute to the understanding of the disease. For more information on these trials, you can visit ClinicalTrials.gov and search for 'central neurocytoma'. Engaging in clinical trials may provide access to cutting-edge therapies and contribute to advancing knowledge about this rare tumor.
Actionable guidance for navigating care for central neurocytoma
To navigate your care effectively, seek a neurosurgeon with experience in treating brain tumors, particularly central neurocytomas. It may also be beneficial to consult with a neuro-oncologist who specializes in brain tumors. While no patient organizations are currently identified, you can explore resources such as the Genetic and Rare Diseases Information Center (GARD) at rarediseases.info.nih.gov for additional support and information. Participating in clinical trials could also be a valuable opportunity for accessing new treatments.
Consider asking your healthcare providers these condition-specific questions
Helpful links for rare disease information and support
Clinical profile data for this condition is not yet available. Phenotype information may still be loading below.
Research studies investigating treatments and therapies for this condition.
Active Trials
Total Trials
Data from ClinicalTrials.gov Jan 8, 2026
Consider asking your healthcare providers these condition-specific questions
European rare disease database
Genetic and Rare Diseases Info Center
AI-Generated Content: This summary was generated using AI. Content has been fact-checked. Always consult with qualified healthcare providers for medical guidance.
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Organizations with orphan designations or approved therapies for this disease