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atypical lichen myxedematosus - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

atypical lichen myxedematosus

MONDO:0019447

Also known as:Intermediate lichen myxedematosus

Overview

Atypical lichen myxedematosus is an intermediate form of lichen myxedematosus (LM) (a form of mucin dermal deposit) which does not meet the criteria for either scleromyxedema or the localized form. Three clinical subtypes have been described and include scleromyxedema without monoclonal gammopathy; localized forms with monoclonal gammopathy and/or systemic symptoms; localized forms with mixed features of the 5 subtypes of localized LM (discrete form, acral persistent papular mucinosis, self-healing papular mucinosis, papular mucinosis of infancy, and a pure nodular form). The course of atypical LM is unpredictable because only a few cases have been reported.

ResearchLimited published research (5 articles)

Prognosis

Estimated prevalence: <1 in 1,000,000 (VERY_RARE).

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

No clinical trials have been registered for atypical lichen myxedematosus.

5 publications have been identified in PubMed for atypical lichen myxedematosus. Research spans Case Report / Case Series (100%).

Recent Publications

Marani A (2026). [PMID: 40371822](https://pubmed.ncbi.nlm.nih.gov/40371822/). *Dermatol Reports*. [Case Report / Case Series]
Ghaleb M (2025). [PMID: 41311429](https://pubmed.ncbi.nlm.nih.gov/41311429/). *Oxf Med Case Reports*. [Case Report / Case Series]
Peshin S (2024). [PMID: 39070368](https://pubmed.ncbi.nlm.nih.gov/39070368/). *Cureus*. [Case Report / Case Series]
Bregvadze K (2024). [PMID: 39399580](https://pubmed.ncbi.nlm.nih.gov/39399580/). *SAGE Open Med Case Rep*. [Case Report / Case Series]
Cline E (2024). [PMID: 39628746](https://pubmed.ncbi.nlm.nih.gov/39628746/). *Cureus*. [Case Report / Case Series]

Data assembled from 3 of 12 sources · Last updated Sep 19, 2026, 6:58 PM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

Orphanet

European rare disease database

Orphanet:86797

GARD

Genetic and Rare Diseases Info Center

GARD:19066

Questions for Your Care Team

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atypical lichen myxedematosus

Overview

Prognosis

Research Landscape

Recent Publications

Medical References

External Resources

Orphanet

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team