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TEMPI syndrome is a rare multi-systemic disease characterized by the presence of Telangiectasias, Erythrocytosis with elevated erythropoietin levels, Monoclonal gammopathy, Perinephric-fluid collections, and Intrapulmonary shunting.
Estimated prevalence: <1 in 1,000,000 (VERY_RARE).
No clinical trials have been registered for tempi syndrome.
105 publications have been identified in PubMed for tempi syndrome. Kisho has analyzed 27 by research type. Research spans Review / Meta-Analysis (63%), Other (19%), and Case Report / Case Series (19%).
Research Type | Count | % of Total |
|---|---|---|
Research summaries | 17 | 63% |
Data assembled from 3 of 12 sources · Last updated Sep 19, 2026, 12:49 AM UTC
European rare disease database
Genetic and Rare Diseases Info Center
5 |
19% |
Patient case studies | 5 | 19% |
Adam Z (2026). [PMID: 42172113](https://pubmed.ncbi.nlm.nih.gov/42172113/). *Klin Onkol*. [Review / Meta-Analysis]
Giri S (2026). [PMID: 41019147](https://pubmed.ncbi.nlm.nih.gov/41019147/). *J Clin Exp Hepatol*. [Review / Meta-Analysis]
Sra MS (2026). [PMID: 42215470](https://pubmed.ncbi.nlm.nih.gov/42215470/). *Blood Cancer J*. [Review / Meta-Analysis]
Mir TH (2026). [PMID: 41740896](https://pubmed.ncbi.nlm.nih.gov/41740896/). *J Am Acad Dermatol*. [Other]
Nepal S (2026). [PMID: 32119505](https://pubmed.ncbi.nlm.nih.gov/32119505/). *Unknown Journal*. [Other]
Elshaer M (2025). [PMID: 41180787](https://pubmed.ncbi.nlm.nih.gov/41180787/). *World J Gastroenterol*. [Other]
Adam Z (2025). [PMID: 40962507](https://pubmed.ncbi.nlm.nih.gov/40962507/). *Klin Onkol*. [Review / Meta-Analysis]
Chen J (2025). [PMID: 40344298](https://pubmed.ncbi.nlm.nih.gov/40344298/). *J Cell Mol Med*. [Review / Meta-Analysis]
Patel RK (2025). [PMID: 39325211](https://pubmed.ncbi.nlm.nih.gov/39325211/). *Abdom Radiol (NY)*. [Review / Meta-Analysis]
Marchak K (2025). [PMID: 41242843](https://pubmed.ncbi.nlm.nih.gov/41242843/). *Tech Vasc Interv Radiol*. [Review / Meta-Analysis]