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diffuse panbronchiolitis (DPb) - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

diffuse panbronchiolitis

MONDO:0011490

Also known as:DPbPBLTpanbronchiolitis, diffuse

Overview

Diffuse panbronchiolitis is a rare chronic inflammatory obstructive pulmonary disease primarily affecting the respiratory bronchioles throughout both lungs and inducing sinobronchial infection. Onset occurs in the second to fifth decade of life and manifests by chronic cough, exertional dyspnea, and sputum production. Most patients also have chronic paranasal sinusitis

Clinical Presentation

Features include: Rhonchi, Crackles, Foam cells, and Bronchiectasis and 3 more.

Organ System	Phenotype Count	Example Features
Lungs and breathing	3	Bronchiectasis, Wheezing, Low blood oxygen levels (hypoxemia)

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Diagnosis

Biomarker and diagnostic research for diffuse panbronchiolitis has been reported in the published literature.

Prognosis

Estimated prevalence: <1 in 1,000,000 (VERY_RARE).

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

No clinical trials have been registered for diffuse panbronchiolitis.

18 publications have been identified in PubMed for diffuse panbronchiolitis. Research spans Case Report / Case Series (67%), Epidemiology / Natural History (11%), and Other (6%).

Research Type	Count	% of Total
Patient case studies	12	67%

Data assembled from 5 of 12 sources · Last updated Sep 20, 2026, 8:40 AM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

OMIM

Online Mendelian Inheritance in Man

OMIM:604809

Orphanet

European rare disease database

Orphanet:171700

GARD

Genetic and Rare Diseases Info Center

GARD:8526

Questions for Your Care Team

→Are there specialists or centers of excellence for this condition in my area?
→Is there a patient registry I should consider joining?

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diffuse panbronchiolitis

Overview

Clinical Presentation

Explore clinical features

Diagnosis

Prognosis

Research Landscape

Medical References

External Resources

OMIM

Orphanet

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

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