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pulmonary nodular lymphoid hyperplasia - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

pulmonary nodular lymphoid hyperplasia

MONDO:0008348

Also known as:pulmonary pseudolymphomapulmonary nodular lymphoid hyperplasia, familial

Overview

Pulmonary nodular lymphoid hyperplasia (PNHL) is a reactive lymphoid proliferation manifesting as solitary or multiple nodules in the lung.

ResearchLimited published research (5 articles)

Clinical Presentation

Built from Human Phenotype Ontology (HPO) phenotype annotations and GeneReviews clinical descriptions. Features represent findings documented across known cases — not an exhaustive list of possible symptoms.

Features include common findings: Follicular hyperplasia, Cough, Nodular pattern on pulmonary HRCT, and Plasmacytosis and others; and sometimes findings: Dyspnea, Ground-glass opacification, and Chest pain. 10 total HPO annotations.

Organ System	Phenotype Count	Example Features
Lungs and breathing	2	Nodular pattern on pulmonary HRCT, Dyspnea

Diagnosis

Biomarker and diagnostic research for pulmonary nodular lymphoid hyperplasia has been reported in the published literature.

Prognosis

Phenotype severity distribution: 5 common features.

Estimated prevalence: Unknown (Unknown prevalence).

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

No clinical trials have been registered for pulmonary nodular lymphoid hyperplasia.

6 publications have been identified in PubMed for pulmonary nodular lymphoid hyperplasia. Research spans Case Report / Case Series (60%), Diagnostic / Biomarker (20%), and Basic Science / Preclinical (20%).

Recent Publications

Yamano T (2026). [PMID: 41808908](https://pubmed.ncbi.nlm.nih.gov/41808908/). *Respirol Case Rep*. [Case Report / Case Series]
Nie DL (2025). [PMID: 39129435](https://pubmed.ncbi.nlm.nih.gov/39129435/). *J Thorac Imaging*. [Diagnostic / Biomarker]
Schneider Galvão G (2025). [PMID: 41404299](https://pubmed.ncbi.nlm.nih.gov/41404299/). *Lung Cancer (Auckl)*. [Case Report / Case Series]
Bhattarai N (2025). [PMID: 40587389](https://pubmed.ncbi.nlm.nih.gov/40587389/). *Am J Clin Pathol*. [Basic Science / Preclinical]
Wang XB (2024). [PMID: 39653539](https://pubmed.ncbi.nlm.nih.gov/39653539/). *Zhonghua Jie He He Hu Xi Za Zhi*. [Case Report / Case Series]

Data assembled from 5 of 12 sources · Last updated Sep 19, 2026, 6:54 PM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

OMIM

Online Mendelian Inheritance in Man

OMIM:178610

Orphanet

European rare disease database

Orphanet:60026

GARD

Genetic and Rare Diseases Info Center

GARD:16663

Questions for Your Care Team

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Kisho

pulmonary nodular lymphoid hyperplasia

Overview

Clinical Presentation

Diagnosis

Prognosis

Research Landscape

Recent Publications

Medical References

External Resources

OMIM

Orphanet

GARD

Questions for Your Care Team

Questions for Your Care Team

Explore clinical features

Latest News & Developments

Nodular Pulmonary Amyloidosis Associated With Sjögren's Syndrome.

pulmonary nodular lymphoid hyperplasia

Overview

Clinical Presentation

Diagnosis

Prognosis

Research Landscape

Recent Publications

Medical References

External Resources

OMIM

Orphanet

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

Explore clinical features

Latest News & Developments

Nodular Pulmonary Amyloidosis Associated With Sjögren's Syndrome.