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A rare variant of malignant peripheral nerve sheath tumor composed predominantly or exclusively of epithelioid cells.
Biomarker and diagnostic research for epithelioid malignant peripheral nerve sheath tumor has been reported in the published literature.
1 clinical trial registered. Interventions under study include drug therapy and procedural interventions. Pipeline includes 1 PHASE2. Research is primarily sponsored by academic and government institutions.
22 publications have been identified in PubMed for epithelioid malignant peripheral nerve sheath tumor. Research spans Case Report / Case Series (73%), Diagnostic / Biomarker (14%), and Review / Meta-Analysis (5%).
Research Type | Count | % of Total |
|---|---|---|
Patient case studies | 16 |
Data assembled from 3 of 12 sources · Last updated Sep 18, 2026, 8:00 AM UTC
Testing and diagnosis research | 3 | 14% |
Research summaries | 1 | 5% |
Laboratory research | 1 | 5% |
Disease patterns and progression | 1 | 5% |
Richman LP (2026). [PMID: 41881192](https://pubmed.ncbi.nlm.nih.gov/41881192/). *Mod Pathol*. [Diagnostic / Biomarker]
García Pastor EM (2026). [PMID: 41547237](https://pubmed.ncbi.nlm.nih.gov/41547237/). *Rev Esp Patol*. [Case Report / Case Series]
Deng Y (2026). [PMID: 41817562](https://pubmed.ncbi.nlm.nih.gov/41817562/). *Clin Nucl Med*. [Case Report / Case Series]
Gupta N (2026). [PMID: 41400020](https://pubmed.ncbi.nlm.nih.gov/41400020/). *Diagn Cytopathol*. [Case Report / Case Series]
Mori T (2026). [PMID: 41571450](https://pubmed.ncbi.nlm.nih.gov/41571450/). *J Clin Pathol*. [Basic Science / Preclinical]
Shirai Y (2026). [PMID: 40653799](https://pubmed.ncbi.nlm.nih.gov/40653799/). *Int J Surg Pathol*. [Case Report / Case Series]
Spencer-Taylor A (2026). [PMID: 42027815](https://pubmed.ncbi.nlm.nih.gov/42027815/). *Front Vet Sci*. [Case Report / Case Series]
Porche K (2026). [PMID: 41237389](https://pubmed.ncbi.nlm.nih.gov/41237389/). *J Neurosurg*. [Case Report / Case Series]
Aldakak MA (2026). [PMID: 42261332](https://pubmed.ncbi.nlm.nih.gov/42261332/). *Cancer Manag Res*. [Case Report / Case Series]
Ward M (2025). [PMID: 39941585](https://pubmed.ncbi.nlm.nih.gov/39941585/). *J Clin Med*. [Diagnostic / Biomarker]
AI-curated news mentioning epithelioid malignant peripheral nerve sheath tumor
Updated Sep 13, 2026
Research reveals that molecular subgroups of human malignant peripheral nerve sheath tumors are conserved in canines, suggesting potential for comparative studies in treatment and understanding of this rare tumor type. This finding may enhance translational research efforts between species.
A recent study highlights a case of malignant peripheral nerve sheath tumor (MPNST) found in an adrenal incidentaloma, emphasizing the need for awareness of this rare pathology. This discovery could influence diagnostic approaches for adrenal tumors.
A case report details a rare instance of cytokeratin-positive pleomorphic chest wall sarcoma that mimicked malignant peripheral nerve sheath tumor (MPNST). This discovery may enhance diagnostic accuracy for similar sarcomas.