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immunotactoid or fibrillary glomerulopathy - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

immunotactoid or fibrillary glomerulopathy

MONDO:0019605

Also known as:Immunotactoid or fibrillary glomerulonephritisfibrillary glomerulonephritis and immunotactoid glomerulopathy

Overview

A group of very rare glomerular diseases, composed of immunotactoid glomerulopathy (ITG) and non-amyloid fibrillary glomerulopathy (non-amyloid FGP), that are characterized by mesangial deposition of monoclonal microtubular or polyclonal fibrillar deposits. Both present clinically with nephrotic range proteinuria, hematuria and renal insufficiency leading to renal failure in many cases. ITG is more likely to manifest with underlying lymphoproliferative disease, hypocomplementemia, dysproteinemia, monoclonal gammopathy or occult cryoglobulinemia. Non-amyloid FGP is 10 times more frequent than ITG.

Diagnosis

Biomarker and diagnostic research for immunotactoid or fibrillary glomerulopathy has been reported in the published literature.

Prognosis

Estimated prevalence: <1 in 1,000,000 (VERY_RARE).

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

No clinical trials have been registered for immunotactoid or fibrillary glomerulopathy.

78 publications have been identified in PubMed for immunotactoid or fibrillary glomerulopathy. Research spans Case Report / Case Series (63%), Review / Meta-Analysis (13%), and Epidemiology / Natural History (10%).

Research Type	Count	% of Total
Patient case studies	49	63%

Data assembled from 3 of 12 sources · Last updated Sep 19, 2026, 9:40 PM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

Orphanet

European rare disease database

Orphanet:91137

GARD

Genetic and Rare Diseases Info Center

GARD:12741

Questions for Your Care Team

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immunotactoid or fibrillary glomerulopathy

Overview

Diagnosis

Prognosis

Research Landscape

Medical References

External Resources

Orphanet

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

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