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inflammatory pseudotumor of the liver - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

inflammatory pseudotumor of the liver

MONDO:0019528

Also known as:IgG4-related hepatopathy

Overview

Inflammatory pseudotumor (IPT) of the liver is a rare benign tumor-like lesion.

ResearchLimited published research (5 articles)

Clinical Presentation

Built from Human Phenotype Ontology (HPO) phenotype annotations and GeneReviews clinical descriptions. Features represent findings documented across known cases — not an exhaustive list of possible symptoms.

Features include always present findings: Neoplasm of the liver and Abnormal liver sonography; and common findings: Fever, Abdominal pain, and Autoimmune antibody positivity. 16 total HPO annotations.

Organ System	Phenotype Count	Example Features
Digestive system	9	Neoplasm of the liver, Abnormal liver sonography, Abdominal pain

Prognosis

Phenotype severity distribution: 2 always present features, 3 common features.

Estimated prevalence: Unknown (Unknown prevalence).

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

No clinical trials have been registered for inflammatory pseudotumor of the liver.

5 publications have been identified in PubMed for inflammatory pseudotumor of the liver. Research spans Case Report / Case Series (60%) and Review / Meta-Analysis (40%).

Recent Publications

Higuchi Y (2026). [PMID: 41822346](https://pubmed.ncbi.nlm.nih.gov/41822346/). *Med Int (Lond)*. [Case Report / Case Series]
Beuers U (2025). [PMID: 40342085](https://pubmed.ncbi.nlm.nih.gov/40342085/). *Semin Liver Dis*. [Review / Meta-Analysis]
Zhao Z (2025). [PMID: 41267878](https://pubmed.ncbi.nlm.nih.gov/41267878/). *Front Med (Lausanne)*. [Case Report / Case Series]
Zengin A (2024). [PMID: 39917402](https://pubmed.ncbi.nlm.nih.gov/39917402/). *Turk J Surg*. [Case Report / Case Series]
Barabino M (2024). [PMID: 39272784](https://pubmed.ncbi.nlm.nih.gov/39272784/). *Cancers (Basel)*. [Review / Meta-Analysis]

Data assembled from 4 of 12 sources · Last updated Sep 20, 2026, 7:58 AM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

Orphanet

European rare disease database

Orphanet:90003

GARD

Genetic and Rare Diseases Info Center

GARD:19098

Questions for Your Care Team

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inflammatory pseudotumor of the liver

Overview

Clinical Presentation

Prognosis

Research Landscape

Recent Publications

Medical References

External Resources

Orphanet

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

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