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low grade fibromyxoid sarcoma - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

low grade fibromyxoid sarcoma

MONDO:0006272

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Overview

A low grade, late-metastasizing variant of fibrosarcoma characterized by alternating fibrous and myxoid areas and a whorling growth pattern. The neoplastic cells have a spindle morphology, and lack hyperchromasia or significant nuclear atypia. Approximately 40% of cases show the focal presence of collagen rosettes. A t(7;16)(q33;p11) translocation has been identified in the majority of cases, associated with the presence of FUS-CREB3L2 fusion protein. Rare cases carry the t(11;16)(p11;p11) translocation which is associated with the presence of the FUS-CREB3L1 fusion protein.

Clinical Trials4 registered · 3 recruiting

Diagnosis

Biomarker and diagnostic research for low grade fibromyxoid sarcoma has been reported in the published literature.

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

4 clinical trials registered, 3 recruiting. Interventions under study include drug therapy, other interventions, and procedural interventions. Pipeline includes 2 PHASE2, 1 PHASE1, 1 NA. Research is primarily sponsored by academic and government institutions.

39 publications have been identified in PubMed for low grade fibromyxoid sarcoma. Research spans Case Report / Case Series (56%), Diagnostic / Biomarker (21%), and Basic Science / Preclinical (10%).

Research Type	Count	% of Total
Patient case studies	22

Data assembled from 3 of 12 sources · Last updated Sep 19, 2026, 4:31 PM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

Questions for Your Care Team

→Are any of the 4 active clinical trials a good fit for my situation?
→Are there specialists or centers of excellence for this condition in my area?
→Is there a patient registry I should consider joining?

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Kisho

low grade fibromyxoid sarcoma

Overview

Diagnosis

Research Landscape

Medical References

Questions for Your Care Team

Questions for Your Care Team

Recent Publications

Latest News & Developments

Low-grade fibromyxoid sarcoma in abdominopelvic and retroperitoneal locations: a clinicopathologic analysis of 26 cases and a review of the literature.

low grade fibromyxoid sarcoma

Overview

Diagnosis

Research Landscape

Medical References

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

Recent Publications

Latest News & Developments

Low-grade fibromyxoid sarcoma in abdominopelvic and retroperitoneal locations: a clinicopathologic analysis of 26 cases and a review of the literature.