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A malignant neoplasm arising from the deep soft tissues in children. It is characterized by the presence of spindle-shaped fibroblasts and collagenous stroma formation in a herringbone growth pattern.
Biomarker and diagnostic research for pediatric fibrosarcoma has been reported in the published literature.
23 clinical trials registered, 12 recruiting. Interventions under study include drug therapy, procedural interventions, other interventions, and biologic therapy. Pipeline includes 1 PHASE3, 12 PHASE2, 6 PHASE1. Research is sponsored by a mix of industry and academic institutions.
NCT ID | Title | Phase | Sponsor | Status |
|---|---|---|---|---|
[NCT06239272](https://clinicaltrials.gov/study/NCT06239272) |
Data assembled from 3 of 12 sources · Last updated Sep 19, 2026, 5:31 AM UTC
NRSTS2021, A Risk Adapted Study Evaluating Maintenance Pazopanib, Limited Margin, Dose-Escalated Radiation Therapy and Selinexor in Non-Rhabdomyosarcoma Soft Tissue Sarcoma (NRSTS) |
PHASE1 |
St. Jude Children's Research Hospital |
RECRUITING |
[NCT06849986](https://clinicaltrials.gov/study/NCT06849986) | IO Combined With AI as First-line Treatment for Patients With Soft Tissue Sarcoma(TAIS) | PHASE2 | Fudan University | RECRUITING |
[NCT06638931](https://clinicaltrials.gov/study/NCT06638931) | Agnostic Therapy in Rare Solid Tumors | PHASE2 | Instituto do Cancer do Estado de São Paulo | RECRUITING |
[NCT07173972](https://clinicaltrials.gov/study/NCT07173972) | Dose-escalated, Hypofractionated, Definitive Proton Radiotherapy for Patients With Inoperable Soft Tissue Sarcoma. | PHASE2 | Oslo University Hospital | RECRUITING |
[NCT05253131](https://clinicaltrials.gov/study/NCT05253131) | Trial of Selumetinib and Bromodomain Inhibitor With Durvalumab for Sarcomas | PHASE2 | University of Alabama at Birmingham | RECRUITING |
145 publications have been identified in PubMed for pediatric fibrosarcoma. Research spans Basic Science / Preclinical (36%), Review / Meta-Analysis (23%), and Case Report / Case Series (17%).
Research Type | Count | % of Total |
|---|---|---|
Laboratory research | 52 | 36% |
Research summaries | 34 | 23% |
Patient case studies | 24 | 17% |
Clinical study results | 10 | 7% |
New treatment approaches | 10 | 7% |
Disease patterns and progression | 8 | 6% |
Testing and diagnosis research | 6 | 4% |
Other research | 1 | 1% |
Thomas G (2026). [PMID: 41587909](https://pubmed.ncbi.nlm.nih.gov/41587909/). *The Journal of small animal practice*. [Case Report / Case Series]
Kitagawa Y (2026). [PMID: 41908147](https://pubmed.ncbi.nlm.nih.gov/41908147/). *Neurooncol Adv*. [Basic Science / Preclinical]
Fan N (2026). [PMID: 42180617](https://pubmed.ncbi.nlm.nih.gov/42180617/). *Oncol Lett*. [Basic Science / Preclinical]
Popović KJ (2026). [PMID: 41901254](https://pubmed.ncbi.nlm.nih.gov/41901254/). *Pharmaceuticals (Basel)*. [Basic Science / Preclinical]
Ibáñez-Navarro A (2026). [PMID: 41982953](https://pubmed.ncbi.nlm.nih.gov/41982953/). *Transl Pediatr*. [Other]
Saitoh Y (2026). [PMID: 41587625](https://pubmed.ncbi.nlm.nih.gov/41587625/). *Biochim Biophys Acta Gen Subj*. [Basic Science / Preclinical]
Wang Y (2026). [PMID: 41783920](https://pubmed.ncbi.nlm.nih.gov/41783920/). *Mater Horiz*. [Basic Science / Preclinical]
Chen J (2026). [PMID: 41455473](https://pubmed.ncbi.nlm.nih.gov/41455473/). *Immunity*. [Basic Science / Preclinical]
Miyashi Y (2026). [PMID: 41617463](https://pubmed.ncbi.nlm.nih.gov/41617463/). *Anticancer Res*. [Diagnostic / Biomarker]
LaDouceur EEB (2026). [PMID: 41772860](https://pubmed.ncbi.nlm.nih.gov/41772860/). *Vet Clin Pathol*. [Basic Science / Preclinical]