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neurofibrosarcoma - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

neurofibrosarcoma

MONDO:0002675

Also known as:neurosarcomaneurosarcoma [obs]

Find Clinical TrialsTrials

Overview

A malignant tumor that arises from small cutaneous nerves, is locally aggressive, and has a potential for metastasis. Characteristic histopathologic features include proliferating atypical spindle cells with slender wavy and pointed nuclei, hypocellular areas, and areas featuring organized whorls of fibroblastic proliferation. The most common primary sites are the extremities, retroperitoneum, and trunk. These tumors tend to present in childhood, often in association with neurofibromatosis 1. (From DeVita et al., Cancer: Principles & Practice of Oncology, 5th ed, p1662; Mayo Clin Proc 1990 Feb;65(2):164-72)

Clinical Trials6 registered · 4 recruiting

Diagnosis

Biomarker and diagnostic research for neurofibrosarcoma has been reported in the published literature.

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

6 clinical trials registered, 4 recruiting. Interventions under study include drug therapy, other interventions, procedural interventions, and biologic therapy. Pipeline includes 5 PHASE2, 1 NA. Research is sponsored by a mix of industry and academic institutions.

NCT ID	Title	Phase	Sponsor	Status
[NCT06638931](https://clinicaltrials.gov/study/NCT06638931)

Data assembled from 3 of 12 sources · Last updated Oct 3, 2026, 1:35 PM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

GARD

Genetic and Rare Diseases Info Center

GARD:8211

Questions for Your Care Team

→Are any of the 6 active clinical trials a good fit for my situation?
→Are there specialists or centers of excellence for this condition in my area?
→Is there a patient registry I should consider joining?

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Research Type	Count	% of Total
Laboratory research	15	36%
Patient case studies	12	29%
Research summaries	4	10%
Clinical study results	4	10%
Testing and diagnosis research	3	7%
Disease patterns and progression	3	7%
New treatment approaches	1	2%

neurofibrosarcoma

Overview

Diagnosis

Research Landscape

Medical References

External Resources

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

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