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onychocytic matricoma - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

onychocytic matricoma

MONDO:0017586

Also known as:acanthoma of the nail matrix

Overview

Onychocytic matricoma is a rare tumor of the nail that is generally benign. Affected people often experience thickening of the involved portion of the nail. The tumor may be pigmented (melanonychia - a black or brown pigmentation of the normal nail plate) or non-pigmented. The exact underlying cause of onychocytic matricoma is currently unknown. It generally occurs sporadically in people with no family history of the condition. Treatment generally consists of surgical excision.

ResearchLimited published research (9 articles)

Diagnosis

Biomarker and diagnostic research for onychocytic matricoma has been reported in the published literature.

Prognosis

Estimated prevalence: <1 in 1,000,000 (VERY_RARE).

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

No clinical trials have been registered for onychocytic matricoma.

9 publications have been identified in PubMed for onychocytic matricoma. Research spans Case Report / Case Series (44%), Diagnostic / Biomarker (22%), and Epidemiology / Natural History (22%).

Recent Publications

Perrin C (2026). [PMID: 41283671](https://pubmed.ncbi.nlm.nih.gov/41283671/). *The American Journal of dermatopathology*. [Case Report / Case Series]
Nayak A (2026). [PMID: 41983749](https://pubmed.ncbi.nlm.nih.gov/41983749/). *Indian J Pathol Microbiol*. [Case Report / Case Series]
Perrin C (2026). [PMID: 42012242](https://pubmed.ncbi.nlm.nih.gov/42012242/). *Am J Dermatopathol*. [Case Report / Case Series]
Tordjman L (2025). [PMID: 40064603](https://pubmed.ncbi.nlm.nih.gov/40064603/). *International journal of dermatology*. [Epidemiology / Natural History]
Scandiuzzi Maciel E (2025). [PMID: 39727317](https://pubmed.ncbi.nlm.nih.gov/39727317/). *Dermatologic surgery : official publication for American Society for Dermatologic Surgery [et al.]*. [Diagnostic / Biomarker]

Data assembled from 3 of 12 sources · Last updated Sep 20, 2026, 9:41 AM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

Orphanet

European rare disease database

Orphanet:300504

GARD

Genetic and Rare Diseases Info Center

GARD:11007

Questions for Your Care Team

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onychocytic matricoma

Overview

Diagnosis

Prognosis

Research Landscape

Recent Publications

Medical References

External Resources

Orphanet

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team