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postlingual non-syndromic genetic hearing loss - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

postlingual non-syndromic genetic hearing loss

MONDO:0016298

Also known as:isolated postlingual genetic deafnesspostlingual non-syndromic genetic deafness

Overview

Postlingual non-syndromic genetic deafness is a rare, genetically highly heterogeneous otorhinolaryngologic disease, resulting from inner and/or middle ear or hearing nerve anomalies, typically characterized by progressive, bilateral, moderate to profound hearing loss (mean sensorineural hearing impairment equal to 40 dB or more for 500-, 1,000-, and 2,000-Hz frequency tones in the better ear) which occurs after the onset of speech development and is not associated with visible external ear abnormalities or any other medical problems. Language development is not initially significantly delayed.

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

No clinical trials have been registered for postlingual non-syndromic genetic hearing loss.

13 publications have been identified in PubMed for postlingual non-syndromic genetic hearing loss. Research spans Basic Science / Preclinical (54%), Case Report / Case Series (38%), and Review / Meta-Analysis (8%).

Research Type	Count	% of Total
Laboratory research	7	54%

Data assembled from 3 of 12 sources · Last updated Sep 18, 2026, 10:32 PM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

Orphanet

European rare disease database

Orphanet:216452

Questions for Your Care Team

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postlingual non-syndromic genetic hearing loss

Overview

Research Landscape

Medical References

External Resources

Orphanet

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

Recent Publications