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right superior vena cava connecting to left-sided atrium - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

right superior vena cava connecting to left-sided atrium

MONDO:0020441

Also known as:right SVC connecting to left-sided atriumright superior caval vein connecting to left-sided atrium

Overview

Right superior vena cava connecting to the left-sided atrium is a rare, congenital vascular malformation of the major vessels characterized by the right SVC passing medially and dorsally to the aortic root and draining into the left atrium. Patients usually present a right-to-left systemic venous blood shunt which may manifest with arterial hypoxemia, cyanosis, exercise dyspnea, clubbing of the fingers, palpitations, murmurs and/or potentially fatal brain abscess. Association with other cardiac anomalies has been reported.

ResearchLimited published research (5 articles)

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

No clinical trials have been registered for right superior vena cava connecting to left-sided atrium.

5 publications have been identified in PubMed for right superior vena cava connecting to left-sided atrium. Research spans Case Report / Case Series (80%) and Clinical Trial Publication (20%).

Recent Publications

Alali JM (2026). [PMID: 41889475](https://pubmed.ncbi.nlm.nih.gov/41889475/). *Radiology case reports*. [Case Report / Case Series]
Pishdad P (2026). [PMID: 41503110](https://pubmed.ncbi.nlm.nih.gov/41503110/). *Radiology case reports*. [Case Report / Case Series]
Fan F (2025). [PMID: 40012311](https://pubmed.ncbi.nlm.nih.gov/40012311/). *Cardiology in the young*. [Clinical Trial Publication]
Nash TR (2025). [PMID: 40682498](https://pubmed.ncbi.nlm.nih.gov/40682498/). *Australian veterinary journal*. [Case Report / Case Series]
Tej U (2024). [PMID: 39071540](https://pubmed.ncbi.nlm.nih.gov/39071540/). *European heart journal. Case reports*. [Case Report / Case Series]

Data assembled from 3 of 12 sources · Last updated Sep 20, 2026, 5:01 PM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

Orphanet

European rare disease database

Orphanet:99110

GARD

Genetic and Rare Diseases Info Center

GARD:19653

Questions for Your Care Team

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right superior vena cava connecting to left-sided atrium

Overview

Research Landscape

Recent Publications

Medical References

External Resources

Orphanet

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team