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extraventricular neurocytoma (EVN) - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

extraventricular neurocytoma

MONDO:0016727

Also known as:EVNextraventricular neurocytoma (WHO grade II)

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Overview

Extraventricular neurocytoma (EVN), a variant of central neurocytoma, is a rare neuronal neoplasm, composed of round cells with neuronal differentiation, which is located outside of the ventricular system, usually within the spinal cord or cerebral hemispheres and that manifests with headache, nausea, vomiting, complex partial seizures or focal neurological deficits. In some cases it may exhibit atypical features consistent with aggressive clinical behavior.

Clinical Trials1 registered

Diagnosis

Biomarker and diagnostic research for extraventricular neurocytoma has been reported in the published literature.

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

1 clinical trial registered. Interventions under study include drug therapy. Pipeline includes 1 PHASE4. Research is primarily industry-sponsored.

13 publications have been identified in PubMed for extraventricular neurocytoma. Research spans Case Report / Case Series (46%), Review / Meta-Analysis (15%), and Basic Science / Preclinical (15%).

Research Type	Count	% of Total
Patient case studies	6	46%

Data assembled from 4 of 12 sources · Last updated Sep 18, 2026, 2:11 PM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

Orphanet

European rare disease database

Orphanet:251927

GARD

Genetic and Rare Diseases Info Center

GARD:20727

Questions for Your Care Team

→Are any of the 1 active clinical trial a good fit for my situation?
→Are there specialists or centers of excellence for this condition in my area?
→Is there a patient registry I should consider joining?

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extraventricular neurocytoma

Overview

Diagnosis

Research Landscape

Medical References

External Resources

Orphanet

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

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