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Idiopathic dilatation of the right atrium (IDRA) is a rare congenital heart malformation of unknown etiology that is characterized by an extremely dilated right atrium, and that is usually asymptomatic and fortuitously discovered by echocardiography or chest radiography, and can be sometimes associated with other anomalies such as atrial arrhythmias (e.g. atrial flutter, atrial fibrillation, supraventricular tachycardia), severe tricuspid regurgitation, or atrial thrombus that could lead to potentially life-threatening thromboembolic complications.
Estimated prevalence: Unknown (Unknown prevalence).
No clinical trials have been registered for familial idiopathic dilatation of the right atrium.
2 publications have been identified in PubMed for familial idiopathic dilatation of the right atrium. Research spans Review / Meta-Analysis (100%).
Muharram M (2026). [PMID: 41582218](https://pubmed.ncbi.nlm.nih.gov/41582218/). *J Med Case Rep*. [Review / Meta-Analysis]
Thiene G (2024). [PMID: 39452271](https://pubmed.ncbi.nlm.nih.gov/39452271/). *J Cardiovasc Dev Dis*. [Review / Meta-Analysis]
Data assembled from 3 of 12 sources · Last updated Sep 20, 2026, 10:20 PM UTC
European rare disease database
Genetic and Rare Diseases Info Center