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Biomarker and diagnostic research for primary central nervous system vasculitis has been reported in the published literature.
Estimated prevalence: Unknown (Unknown prevalence).
No clinical trials have been registered for primary central nervous system vasculitis.
147 publications have been identified in PubMed for primary central nervous system vasculitis. Research spans Case Report / Case Series (39%), Review / Meta-Analysis (23%), and Epidemiology / Natural History (14%).
Research Type | Count | % of Total |
|---|---|---|
Patient case studies | 58 | 39% |
Data assembled from 3 of 12 sources · Last updated Sep 17, 2026, 11:31 PM UTC
European rare disease database
Genetic and Rare Diseases Info Center
Research summaries
34 |
23% |
Disease patterns and progression | 21 | 14% |
Testing and diagnosis research | 13 | 9% |
Clinical study results | 10 | 7% |
Other research | 6 | 4% |
Laboratory research | 5 | 3% |
Hsu CL (2026). [PMID: 41298202](https://pubmed.ncbi.nlm.nih.gov/41298202/). *Pediatr Neonatol*. [Case Report / Case Series]
de Sousa ÍA (2026). [PMID: 41902495](https://pubmed.ncbi.nlm.nih.gov/41902495/). *Headache*. [Review / Meta-Analysis]
Nguyen JV (2026). [PMID: 41489860](https://pubmed.ncbi.nlm.nih.gov/41489860/). *JAMA Neurol*. [Clinical Trial Publication]
Kesav P (2026). [PMID: 41889687](https://pubmed.ncbi.nlm.nih.gov/41889687/). *Vasc Health Risk Manag*. [Review / Meta-Analysis]
Salvarani C (2026). [PMID: 42127334](https://pubmed.ncbi.nlm.nih.gov/42127334/). *Neurol Neuroimmunol Neuroinflamm*. [Case Report / Case Series]
Nehme A (2026). [PMID: 41212528](https://pubmed.ncbi.nlm.nih.gov/41212528/). *Rheumatology (Oxford)*. [Diagnostic / Biomarker]
Rai P (2026). [PMID: 40835417](https://pubmed.ncbi.nlm.nih.gov/40835417/). *AJNR Am J Neuroradiol*. [Review / Meta-Analysis]
Meghashyam S (2026). [PMID: 41270340](https://pubmed.ncbi.nlm.nih.gov/41270340/). *Curr Opin Immunol*. [Review / Meta-Analysis]
Kuroki R (2026). [PMID: 41611325](https://pubmed.ncbi.nlm.nih.gov/41611325/). *BMJ Case Rep*. [Case Report / Case Series]
Gusatovic J (2026). [PMID: 42230004](https://pubmed.ncbi.nlm.nih.gov/42230004/). *BMJ Case Rep*. [Diagnostic / Biomarker]
AI-curated news mentioning primary central nervous system vasculitis
Updated Sep 11, 2026
A real-world retrospective study evaluates the efficacy of telitacicept in treating primary angiitis of the central nervous system. The findings contribute to understanding treatment options for this rare condition.
A case study highlights Balamuthia mandrillaris as a rare cause of central nervous system vasculitis in a young child. This discovery emphasizes the need for awareness and further research into this pathogen's impact on neurological health.
New French guidelines have been published for the diagnosis and management of primary central nervous system vasculitis. These guidelines aim to standardize care and improve outcomes for patients with this rare condition.