Kisho is an information platform, not a medical provider. Nothing on this site constitutes medical advice, diagnosis, or treatment recommendations. All content is aggregated from publicly available sources (including ClinicalTrials.gov, PubMed, FDA.gov, and Orphanet) and is provided for informational purposes only. Clinical trial eligibility, treatment decisions, and any health-related actions should always be discussed with a qualified healthcare professional. Kisho does not endorse any specific therapy, organization, or clinical trial. Terms of use · Privacy policy
Biomarker and diagnostic research for primary central nervous system vasculitis has been reported in the published literature.
Estimated prevalence: Unknown (Unknown prevalence).
No clinical trials have been registered for primary central nervous system vasculitis.
147 publications have been identified in PubMed for primary central nervous system vasculitis. Research spans Case Report / Case Series (39%), Review / Meta-Analysis (23%), and Epidemiology / Natural History (14%).
Research Type | Count | % of Total |
|---|---|---|
Patient case studies | 58 | 39% |
Data assembled from 3 of 12 sources · Last updated Nov 2, 2026, 9:22 PM UTC
European rare disease database
Genetic and Rare Diseases Info Center
Research summaries
34 |
23% |
Disease patterns and progression | 21 | 14% |
Testing and diagnosis research | 13 | 9% |
Clinical study results | 10 | 7% |
Other research | 6 | 4% |
Laboratory research | 5 | 3% |
Hsu CL (2026). [PMID: 41298202](https://pubmed.ncbi.nlm.nih.gov/41298202/). *Pediatr Neonatol*. [Case Report / Case Series]
de Sousa ÍA (2026). [PMID: 41902495](https://pubmed.ncbi.nlm.nih.gov/41902495/). *Headache*. [Review / Meta-Analysis]
Nguyen JV (2026). [PMID: 41489860](https://pubmed.ncbi.nlm.nih.gov/41489860/). *JAMA Neurol*. [Clinical Trial Publication]
Kesav P (2026). [PMID: 41889687](https://pubmed.ncbi.nlm.nih.gov/41889687/). *Vasc Health Risk Manag*. [Review / Meta-Analysis]
Salvarani C (2026). [PMID: 42127334](https://pubmed.ncbi.nlm.nih.gov/42127334/). *Neurol Neuroimmunol Neuroinflamm*. [Case Report / Case Series]
Nehme A (2026). [PMID: 41212528](https://pubmed.ncbi.nlm.nih.gov/41212528/). *Rheumatology (Oxford)*. [Diagnostic / Biomarker]
Rai P (2026). [PMID: 40835417](https://pubmed.ncbi.nlm.nih.gov/40835417/). *AJNR Am J Neuroradiol*. [Review / Meta-Analysis]
Meghashyam S (2026). [PMID: 41270340](https://pubmed.ncbi.nlm.nih.gov/41270340/). *Curr Opin Immunol*. [Review / Meta-Analysis]
Kuroki R (2026). [PMID: 41611325](https://pubmed.ncbi.nlm.nih.gov/41611325/). *BMJ Case Rep*. [Case Report / Case Series]
Gusatovic J (2026). [PMID: 42230004](https://pubmed.ncbi.nlm.nih.gov/42230004/). *BMJ Case Rep*. [Diagnostic / Biomarker]
AI-curated news mentioning primary central nervous system vasculitis
Updated Oct 20, 2026
A recent study reveals that endothelial neo-antigen expression triggers CD8⁺ T cell-driven central nervous system vasculitis, which is further amplified by peripheral immune challenges. This research could provide insights into the mechanisms underlying CNS vasculitis.
A recent study highlights a rare presentation of mixed connective tissue disease (MCTD) as probable central nervous system vasculitis. This discovery may enhance understanding of MCTD's neurological manifestations.
A real-world retrospective study evaluates the efficacy of telitacicept in treating primary angiitis of the central nervous system. The findings contribute to understanding treatment options for this rare condition.