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rapidly progressive primary central nervous system vasculitis - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

rapidly progressive primary central nervous system vasculitis

MONDO:0100248

Also known as:rapidly progressive PCNSV

Overview

A subset of primary central nervous system vasculitis where disease is rapidly progressive after onset that is characterized by bilateral, multiple, large cerebral vessel lesions and multiple CNS infarctions.

Diagnosis

Biomarker and diagnostic research for rapidly progressive primary central nervous system vasculitis has been reported in the published literature.

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

No clinical trials have been registered for rapidly progressive primary central nervous system vasculitis.

21 publications have been identified in PubMed for rapidly progressive primary central nervous system vasculitis. Research spans Case Report / Case Series (76%), Diagnostic / Biomarker (10%), and Review / Meta-Analysis (10%).

Research Type	Count	% of Total
Patient case studies	16	76%

Data assembled from 2 of 12 sources · Last updated Sep 19, 2026, 4:30 PM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

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Kisho

rapidly progressive primary central nervous system vasculitis

Overview

Diagnosis

Research Landscape

Medical References

Questions for Your Care Team

Questions for Your Care Team

Recent Publications

Latest News & Developments

French guidelines for the diagnosis and management of primary central nervous system vasculitis.

Percutaneous transluminal angioplasty for vertebral artery stenosis due to primary central nervous system vasculitis: A case report.

rapidly progressive primary central nervous system vasculitis

Overview

Diagnosis

Research Landscape

Medical References

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

Recent Publications

Latest News & Developments

French guidelines for the diagnosis and management of primary central nervous system vasculitis.

Percutaneous transluminal angioplasty for vertebral artery stenosis due to primary central nervous system vasculitis: A case report.