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supernumerary nostril - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

supernumerary nostril

MONDO:0015389

Also known as:accessory nostrilsupernumerary naris

Overview

Supernumerary nostril is an extremely rare congenital malformation characterized by the presence of one or more accessory nostrils, with or without accessory cartilage, located medially, above, below or laterally to the other nostrils. Unlike in polyrhinia there is no duplication of the nasal septum/cavity. Supernumerary nostril is often associated with other congenital malformations usually of face.

ResearchLimited published research (4 articles)

Clinical Presentation

Built from Human Phenotype Ontology (HPO) phenotype annotations and GeneReviews clinical descriptions. Features represent findings documented across known cases — not an exhaustive list of possible symptoms.

Features include always present findings: Supernumerary naris; and common findings: Abnormality of the face. 7 total HPO annotations.

Organ System	Phenotype Count	Example Features
Head and neck	2	Abnormality of the face, Tessier cleft
Eyes

Prognosis

Phenotype severity distribution: 1 always present feature, 1 common feature.

Estimated prevalence: <1 in 1,000,000 (VERY_RARE).

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

No clinical trials have been registered for supernumerary nostril.

4 publications have been identified in PubMed for supernumerary nostril. Research spans Case Report / Case Series (100%).

Recent Publications

Handoko RE (2026). [PMID: 42219974](https://pubmed.ncbi.nlm.nih.gov/42219974/). *J Laryngol Otol*. [Case Report / Case Series]
Singh DK (2026). [PMID: 41496994](https://pubmed.ncbi.nlm.nih.gov/41496994/). *Ann Med Surg (Lond)*. [Case Report / Case Series]
Hafiz A (2025). [PMID: 40510714](https://pubmed.ncbi.nlm.nih.gov/40510714/). *Natl J Maxillofac Surg*. [Case Report / Case Series]
Jain A (2024). [PMID: 39523504](https://pubmed.ncbi.nlm.nih.gov/39523504/). *Ear Nose Throat J*. [Case Report / Case Series]

Data assembled from 4 of 12 sources · Last updated Sep 19, 2026, 12:48 AM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

Orphanet

European rare disease database

Orphanet:141096

GARD

Genetic and Rare Diseases Info Center

GARD:19946

Questions for Your Care Team

→Are there specialists or centers of excellence for this condition in my area?
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supernumerary nostril

Overview

Clinical Presentation

Prognosis

Research Landscape

Recent Publications

Medical References

External Resources

Orphanet

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

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