Kisho

Kisho is an information platform, not a medical provider. Nothing on this site constitutes medical advice, diagnosis, or treatment recommendations. All content is aggregated from publicly available sources (including ClinicalTrials.gov, PubMed, FDA.gov, and Orphanet) and is provided for informational purposes only. Clinical trial eligibility, treatment decisions, and any health-related actions should always be discussed with a qualified healthcare professional. Kisho does not endorse any specific therapy, organization, or clinical trial. Terms of use · Privacy policy

central neurocytoma - Clinical Profile, Genes & Research | Kisho | Kisho

Rare Disease

central neurocytoma

MONDO:0019134

Also known as:Neurolipocytomacentral neurocytoma (WHO grade II)CNC

Find Clinical TrialsTrials

Overview

Central neurocytoma is a very rare brain tumor of young adults (over 100 cases reported worldwide). It is typically found in the lateral ventricles and occasionally in the third ventricle. Symptoms are those of increased intracranial pressure: headache, nausea and vomiting, drowsiness, vision problems and mental changes. Total removal of the tumor is the therapy of choice. Post-operative prognosis is generally good.

Clinical Trials1 registered

Clinical Presentation

Built from Human Phenotype Ontology (HPO) phenotype annotations and GeneReviews clinical descriptions. Features represent findings documented across known cases — not an exhaustive list of possible symptoms.

Features include always present findings: Hydrocephalus; and very common findings: Intracranial cystic lesion, Abnormal cellular phenotype, and Abnormal lateral ventricle morphology. 19 total HPO annotations.

Organ System	Phenotype Count	Example Features
Brain and nerves	7	Hydrocephalus, Depression, Ataxia

Diagnosis

Biomarker and diagnostic research for central neurocytoma has been reported in the published literature.

Prognosis

Phenotype severity distribution: 1 always present feature, 3 very common features, 8 common features.

Estimated prevalence: Unknown (Unknown prevalence).

Research Landscape

Sourced from ClinicalTrials.gov and PubMed. Publication types are classified using NLM-curated article metadata; research type breakdowns reflect the nature of published work for this disease.

1 clinical trial registered. Interventions under study include drug therapy. Pipeline includes 1 PHASE4. Research is primarily industry-sponsored.

51 publications have been identified in PubMed for central neurocytoma. Research spans Case Report / Case Series (47%), Clinical Trial Publication (12%), and Basic Science / Preclinical (12%).

Research Type	Count	% of Total
Patient case studies	24	47%

Data assembled from 5 of 12 sources · Last updated Sep 19, 2026, 4:30 PM UTC

MONDOHPOClinicalTrials.govFDAPubMedHGNCClinVarClinGenGeneReviewsOrphanetOMIMRUSP

Medical References

External Resources

Orphanet

European rare disease database

Orphanet:73256

GARD

Genetic and Rare Diseases Info Center

GARD:10641

Questions for Your Care Team

→Are any of the 1 active clinical trial a good fit for my situation?
→Are there specialists or centers of excellence for this condition in my area?
→Is there a patient registry I should consider joining?

← Back to All Diseases

Kisho

central neurocytoma

Overview

Clinical Presentation

Diagnosis

Prognosis

Research Landscape

Medical References

External Resources

Orphanet

GARD

Questions for Your Care Team

Questions for Your Care Team

Explore clinical features

Recent Publications

central neurocytoma

Overview

Clinical Presentation

Diagnosis

Prognosis

Research Landscape

Medical References

External Resources

Orphanet

GARD

Related Diseases

Questions for Your Care Team

Questions for Your Care Team

Explore clinical features

Recent Publications