Pancreatic endocrine tumor, also known as pancreatic neuroendocrine tumor (PNET), describes a group of endocrine tumors originating in the pancreas that are usually indolent and benign, but may have t...
Comprehensive, easy-to-understand information about this condition
How we create this content →Research studies investigating treatments and therapies for this condition.
Active Trials
Total Trials
Data from ClinicalTrials.gov Jan 30, 2026
Research studies investigating treatments and therapies for this condition.
Active Trials
Total Trials
Data from ClinicalTrials.gov Jan 30, 2026
The documentation for pancreatic neuroendocrine tumors is limited due to their rarity, affecting only 1-5 in 10,000 individuals. This low prevalence results in fewer systematic clinical studies and a lack of comprehensive data on genetic factors and clinical features. Additionally, the phenotypic variability and overlap with other conditions complicate the characterization of PNETs.
To navigate your care for pancreatic neuroendocrine tumors, consider consulting with an oncologist who specializes in neuroendocrine tumors. They can provide tailored guidance and treatment options. Additionally, you may want to explore clinical trials that could offer access to emerging therapies. The National Organization for Rare Disorders (NORD) provides resources and support at rarediseases.org. Participating in a clinical trial may also provide valuable insights into your condition and contribute to research efforts.
There are currently 164 active clinical trials investigating various aspects of pancreatic neuroendocrine tumors. Notably, cabozantinib is an FDA-approved treatment, while Foslinanib and a modified human adenovirus are among the designated orphan drugs in development. For more information on ongoing trials, visit ClinicalTrials.gov at https://clinicaltrials.gov/search?cond=pancreatic%20neuroendocrine%20tumor.
Actionable guidance for navigating care for pancreatic neuroendocrine tumor
To navigate your care for pancreatic neuroendocrine tumors, consider consulting with an oncologist who specializes in neuroendocrine tumors. They can provide tailored guidance and treatment options. Additionally, you may want to explore clinical trials that could offer access to emerging therapies. The National Organization for Rare Disorders (NORD) provides resources and support at rarediseases.org. Participating in a clinical trial may also provide valuable insights into your condition and contribute to research efforts.
Consider asking your healthcare providers these condition-specific questions
Helpful links for rare disease information and support
Clinical profile data for this condition is not yet available. Phenotype information may still be loading below.
Research studies investigating treatments and therapies for this condition.
Active Trials
Total Trials
Data from ClinicalTrials.gov Jan 30, 2026
Consider asking your healthcare providers these condition-specific questions
European rare disease database
Genetic and Rare Diseases Info Center
AI-Generated Content: This summary was generated using AI. Content has been fact-checked. Always consult with qualified healthcare providers for medical guidance.
Organizations with approved therapies for this disease
No approved therapies yet
Research is ongoing — 23 companies have orphan drug designations for this disease
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